CLINICAL ASPECTS OF PARRY ROMBERG SYNDROME: A CASE REPORT

Abstract

Introduction: progressive hemifacial atrophy, also known as Parry-Romberg syndrome, is a rare degenerative disease, etiology unclear. Is characterized by a slow and progressive atrophy that affects the face unilaterally. Although there is no treatment protocol to beestablished in these cases, however, it is known that surgery should only be made after stability condition. Objective: Report a case of Parry-Romberg syndrome and discuss a general characteristics, etiology, pathophysiology, differential diagnosis and treatment of progressive hemifacial atrophy. Case description: Female patient, 8 years old, with mild enophthalmos in the left eye, nose and chin deviation to the left side, crowding and mandibular anterior crossbite, in orthodontic treatment, two months ago, for crossbite correction and monitoring for evaluation of future therapeutic needs. Conclusion: The multidisciplinary approach of these patients is essential in order to promote a better quality of life, since the disease can cause a major facial deformity.